I've had the typical "Becker" progression pattern. It generally started in my legs (maybe with a few isolated incidents in my hands before that) and spread upward. My legs remained the most severely affected throughout most of my life. Only veryrecently have my hands and upper body been more severely affected than my legs.
You can see a chart of the progression/changes in my myotonia here.
http://www.flickr.com/photos/ilikeneatrocks/4430888529/lightbox/
That chart is really awesome, but as a child around 5 or 6 i had it pretty bad in my legs. Of course i'm 18 and this is when it has been at its worst. I curious what kind of changes my body will go through when it begins to subside. Right now i have a pretty toned body with a lot of definition, which is the only upside to this disease.